A Rare Case of Bilateral and Midline Cleft Palate With Bilateral Macrostomia.
Karoon Agrawal, Gargi Singhal, Chirag Sharma et al.
✦ AI-curated · Sources linked
Case in brief
A 6-day-old girl was evaluated for bilateral macrostomia and micrognathia. Examination showed a complex cleft palate: a midline submucous cleft, a left lateral submucous cleft, and a right lateral cleft with partial soft-palate agenesis. Pierre Robin sequence led clinicians to defer surgery until her airway was stable. Bilateral macrostomia repair was performed at 12 months, followed at 17 months by one-stage correction of the palatal clefts, using a right buccal myomucosal flap to provide oral lining.
What made this case unusual
The combination of bilateral macrostomia with midline and bilateral lateral palatal clefts, including partial soft-palate agenesis, made this presentation notable.
Diagnostic / clinical pearl
Describe clefts involving the lateral palate as lateral cleft palate, including cases variably labeled as oblique clefts or soft-palate agenesis.