Gastric PEComa as a rare cause of upper gastrointestinal bleeding in pediatrics: Case report.
Cecilia De Goycoechea, María S Groppo, Mariana L Racca Elías et al.
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Case in brief
A 7-year-old girl presented with hematemesis and severe anemia. Imaging and digestive endoscopy identified a gastric mass, initially considered a gastrointestinal stromal tumor (GIST). The mass was surgically resected, and pathological examination established the diagnosis of gastric perivascular epithelioid cell tumor (PEComa).
What made this case unusual
The case involved a gastric PEComa in a child, an exceptional site and age group for this rare mesenchymal tumor; its presentation with upper gastrointestinal bleeding and initial resemblance to GIST added diagnostic interest.
Diagnostic / clinical pearl
A gastric mass suspected to be GIST may require pathological examination for definitive diagnosis; PEComa is a differential diagnosis, including in children presenting with hematemesis.