Orbital chordoid meningioma: a rare entity with an aggressive clinical course.
Izlem Ozturan, Irem Koç, Figen Soylemezoglu et al.
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Case in brief
A patient presented with progressive proptosis and visual impairment due to an orbital chordoid meningioma, a rare and aggressive variant. Despite multiple biopsies and radiotherapy, the tumor exhibited locally aggressive behavior, leading to repeated progression and ultimately requiring orbital exenteration. Histopathological analysis confirmed the diagnosis and indicated a high Ki-67 proliferation index.
Diagnostic / clinical pearl
Clinicians should be aware of the aggressive nature and diagnostic challenges associated with orbital chordoid meningioma, as conventional treatments may have limited efficacy.
Why it matters
This case underscores the necessity for long-term surveillance in patients with orbital chordoid meningioma due to its potential for recurrence and aggressive clinical course.