Atypical Cogan's Syndrome Is Common among Japanese Patients: A Case Report and Literature Review in Japan.
Intern MedFeb 10, 2026 (epub)
Takao Nagashima, Toshikatsu Kaburaki
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Case in brief
A 55-year-old Japanese woman presented with fever, headache, vertigo, sensorineural hearing loss, and scleritis. These findings led to a diagnosis of Cogan’s syndrome. Her hearing acuity returned to its previous level after high-dose glucocorticoid treatment, although seven weeks had elapsed since symptom onset.
What made this case unusual
Hearing recovered to its previous level after high-dose glucocorticoids despite treatment beginning seven weeks after onset.
Diagnostic / clinical pearl
Cogan’s syndrome can present with scleritis and sensorineural hearing loss alongside systemic symptoms such as fever and headache; consider the syndrome when these features occur together.