Supracardiac Total Anomalous Pulmonary Venous Connection with Left Main Bronchial Compression in an Infant.
Yinchang Zhang, Yongnan Li, Yong Mao et al.
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Case in brief
A 4-month-old male infant presented with supracardiac total anomalous pulmonary venous connection (TAPVC) and left main bronchial stenosis, alongside a central atrial septal defect and severe pulmonary hypertension. After supportive management, the infant underwent surgical repair of TAPVC and the atrial septal defect. Intraoperative challenges included initial failure to wean from cardiopulmonary bypass due to pulmonary hypertension, which was resolved by fenestrating the atrial septal patch. Postoperatively, imaging showed unobstructed pulmonary venous return and relief of airway compression, with normal growth at 6-month follow-up.
Diagnostic / clinical pearl
The combination of TAPVC and airway stenosis significantly complicates management and increases perioperative risk, necessitating careful preoperative evaluation and timely surgical intervention.