Multidisciplinary management of an older adult with vascular Ehlers-Danlos syndrome and multiple autoimmune comorbidities.
Ali Burianek, Bilal Niazi, Demetra Menoudakos et al.
✦ AI-curated · Sources linked
Case in brief
An early 60s female with vascular Ehlers-Danlos syndrome (vEDS) presented with extensive comorbidities, including systemic lupus erythematosus and rheumatoid arthritis. Over three years, she underwent multiple surgical interventions and required multidisciplinary management for chronic pain and connective tissue fragility. Unlike typical severe cases, she survived into her 60s, demonstrating a broader spectrum of disease severity.
Diagnostic / clinical pearl
Clinicians should recognize that vascular Ehlers-Danlos syndrome can present with a range of severity and may coexist with multiple autoimmune conditions, necessitating a tailored multidisciplinary management approach.
Why it matters
This case underscores the complexities of managing older patients with vEDS and multiple comorbidities, highlighting the need for coordinated care strategies.